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GeneBio Systems

Recombinant Desmin Monoclonal Antibody

Recombinant Desmin Monoclonal Antibody

SKU:AN301317L

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Size::

Storage:Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.

Shipping:Ice bag

Exp date:12 months

Category ID_II:Primary Antibodies

Category ID_III:Recombinant Antibodies;Monoclonal Antibodies

Abbreviation:Desmin

Target Synonym:OTTHUMP;CSM;DES;CSM1;CSM2;LGMD2R;desmin;CMD1I;DESM;FLJ12025;FLJ39719;FLJ41013;FLJ41793;Intermediate filament protein;OTTHUMP00000064865;DES;CDCD3;CMD1F;CMD1I;CSM1;CSM2;DES;DESM;Desmin;FLJ12025;FLJ39719;FLJ41013;FLJ41793;Intermediate filament protein;OTTHUMP00000064865;LGMD1D;LGMD1E

Research Areas:Signal Transduction;Stem Cells;Cancer;Cardiovascular

Conjugation:Unconjugated

Host:Rabbit

Species reactivity:Human;Mouse;Rat

Application:WB

Isotype:IgG,κ

Clonality:Monoclonal;Recombinant

Clone NO.:8C6

UNIProt ID:P17661

Accession:

Background:This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies.

Concentration:0.2 mg/mL

Immunogen:Recombinant Human Desmin protein

Buffer:PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.

Purification method:Protein A

Dilution:WB 1:20000-1:50000

Calculated MW:53 kDa

ObservedMW:53 kDa

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