Recombinant Glucosamine (N-acetyl)-6-Sulfatase/G6S Monoclonal Antibody

SKU: AN300183P

Size::

Storage:This antibody can be stored at 2℃-8℃ for one month without detectable loss of activity. Antibody products are stable for twelve months from date of receipt when stored at -20℃ to -80℃. Preservative-Free. Avoid repeated freeze-thaw cycles.

Shipping:Ice bag

Exp date:12 months

Category ID_II:Primary Antibodies

Category ID_III:Recombinant Antibodies

Abbreviation:GNS

Target Synonym:GNS;G6S;Glucosamine-6-Sulfatase;N-Acetylglucosamine-6-Sulfatase

Research Areas:Tags & Cell Markers;Signal Transduction;Cell Biology;Metabolism

Conjugation:Unconjugated

Host:Rabbit

Species reactivity:Human

Application:WB

Isotype:IgG

Clonality:Rabbit Monoclonal

Clone NO.:4D5

UNIProt ID:P15586

Accession:

Background:The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

Concentration:1 mg/mL

Immunogen:Recombinant Human GNS protein

Buffer:0.2 μm filtered solution in PBS

Purification method:Protein A

Dilution:WB 1:500-1:2000;

Calculated MW:62 kDa

ObservedMW:95 kDa