GeneBio Systems
Recombinant Desmin Monoclonal Antibody
Recombinant Desmin Monoclonal Antibody
SKU:AN301317L
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Storage:Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.
Shipping:Ice bag
Exp date:12 months
Category ID_II:Primary Antibodies
Category ID_III:Recombinant Antibodies;Monoclonal Antibodies
Abbreviation:Desmin
Target Synonym:OTTHUMP;CSM;DES;CSM1;CSM2;LGMD2R;desmin;CMD1I;DESM;FLJ12025;FLJ39719;FLJ41013;FLJ41793;Intermediate filament protein;OTTHUMP00000064865;DES;CDCD3;CMD1F;CMD1I;CSM1;CSM2;DES;DESM;Desmin;FLJ12025;FLJ39719;FLJ41013;FLJ41793;Intermediate filament protein;OTTHUMP00000064865;LGMD1D;LGMD1E
Research Areas:Signal Transduction;Stem Cells;Cancer;Cardiovascular
Conjugation:Unconjugated
Host:Rabbit
Species reactivity:Human;Mouse;Rat
Application:WB
Isotype:IgG,κ
Clonality:Monoclonal;Recombinant
Clone NO.:8C6
UNIProt ID:P17661
Accession:
Background:This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies.
Concentration:0.2 mg/mL
Immunogen:Recombinant Human Desmin protein
Buffer:PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
Purification method:Protein A
Dilution:WB 1:20000-1:50000
Calculated MW:53 kDa
ObservedMW:53 kDa
