GeneBio Systems
GATM Polyclonal Antibody
GATM Polyclonal Antibody
SKU:E-AB-19032
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Size: 200μL
Storage: Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.
Shipping: The product is shipped with ice pack,upon receipt,store it immediately at the temperature recommended.
Exp date: 12 months
Category ID_II: Primary Antibodies
Category ID_III: Polyclonal Antibodies
Abbreviation: GATM
Target Synonym: AGAT;AT;GATM;GATM;Glycine amidinotransferase;Glycine amidinotransferase; mitochondrial;L-arginine:glycine amidinotransferase;mitochondrial;Transamidinase
Research Areas: Cancer;Metabolism;Signal transduction
Conjugation: Unconjugated
Host: Rabbit
Species reactivity: Human;Mouse;Rat
Application: IHC
Isotype: IgG
Clonality: Polyclonal
Clone NO.:
UNIProt ID: P50440
Accession:
Background: This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by cognitive disability, language impairment, and behavioral disorders.
Concentration: 1.26 mg/mL
Immunogen: Fusion protein of human GATM
Buffer: PBS with 0.05% NaN3 and 40% Glycerol,pH7.4
Purification method: Antigen affinity purification
Dilution: IHC 1:50-1:300
Calculated MW:
ObservedMW:
