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GeneBio Systems

Human 2-oxoisovalerate Dehydrogenase Subunit Alpha, Mitochondrial, BCKDHA ELISA Kit

Human 2-oxoisovalerate Dehydrogenase Subunit Alpha, Mitochondrial, BCKDHA ELISA Kit

SKU:E4421Hu

Regular price ¥128,900 JPY
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Size:96 Tests-1 Kit

Background:The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO2. It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).

Research_area:Others

Applications:ELISA

Target_protein:BCKDHA

Reactivity:Human

Assay type:Sandwich

Sensitivity:0.021ng/ml

Detection range:0.05-20ng/ml

Sample type:Serum, plasma or other biological fluids

Full product name:2-Oxoisovalerate Dehydrogenase Subunit Alpha, Mitochondrial

Species:Human

Storage:2-8ºC

Assay time:1h 30m

UniProt accession:P12694

MASS(Da):50,471

GeneID:593

Synonyms:2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial;BCKDE1A;BCKDH E1-alpha;BCKDHA;Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain;MSU;MSUD1;OVD1A

Gene names:BCKDHA

Standard solution:24ng/ml

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