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GeneBio Systems

CLN6 Polyclonal Antibody

CLN6 Polyclonal Antibody

SKU:BT-AP01988

Regular price ¥87,100 JPY
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Size:100μL

Background:CLN6 (ceroid-lipofuscinosis, neuronal 6, late infantile, variant) is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

Research_area:Others

Target_protein:CLN6

applications:WB, IHC-p, ELISA

Reactivity:Human

Clonality:Polyclonal

Clone ID:

Host:Rabbit

Isotype:IgG

Gene Symbol/ Name:CLN6 Antibody

Immunogen:The antiserum was produced against synthesized peptide derived from human AMPK alpha around the phosphorylation site of Thr172. AA range:140-189

Storage:-20°C for 1 year

Purification:The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

Formulation:Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.

Concentration:1 mg/ml

Molecular weight(Da):35919

UniProt accession:Human: Q9NWW5

Synonyms:CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6

GeneID:Human: 54982

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