OTC Antibody - Cat. #: CSB-PA033931

SKU: CSB-PA033931

Size :50ul

Clone Number:

Aliases:EC 2.1.3.3 antibody; MGC129967 antibody; MGC129968 antibody; MGC138856 antibody; OCTD antibody; Ornithine Carbamoyltransferase antibody; Ornithine carbamoyltransferase mitochondrial antibody; Ornithine carbamoyltransferase, mitochondrial antibody; Ornithine transcarbamylase antibody; Otc antibody; OTC_HUMAN antibody; OTCase antibody

Product Type:Polyclonal Antibody

Immunogen Species:Homo sapiens (Human)

UniProt ID:P00480

Immunogen:Fusion protein of Human OTC

Raised in:Rabbit

Species Reactivity:Human, Mouse, Rat

Tested Applications:ELISA, WB, IHC; ELISA:1:2000-1:5000, WB:1:500-1:2000, IHC:1:50-1:200

Background:This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.

Clonality:Polyclonal

Isotype:IgG

Purification Method:Antigen affinity purification

Conjugate:Non-conjugated

Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol

Form:Liquid

Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Target Names:OTC

Research Areas:Tags & Cell Markers;Metabolism;Signal transduction