GeneBio Systems
ALDH6A1 Polyclonal Antibody
ALDH6A1 Polyclonal Antibody
SKU:E-AB-10769
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Size: 200μL
Storage: Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.
Shipping: The product is shipped with ice pack,upon receipt,store it immediately at the temperature recommended.
Exp date: 12 months
Category ID_II: Primary Antibodies
Category ID_III: Polyclonal Antibodies
Abbreviation: ALDH6A1
Target Synonym: 1110038I05Rik;AI314632;Aldehyde dehydrogenase 6 family member A1;Aldehyde dehydrogenase family 6 member A1;Aldehyde dehydrogenase family 6;subfamily A1;ALDH6A1;Malonate semialdehyde dehydrogenase;Malonate-semialdehyde dehydrogenase [acylating];Methylmalonate semialdehyde dehydrogenase [acylating] mitochondrial;Methylmalonate-semialdehyde dehydrogenase [acylating];MGC37325;MGC40271;Mitochondrial acylating methylmalonate semialdehyde dehydrogenase;mitochondrial;MMSA;MMSADHA;MMSDH
Research Areas: Cancer;Metabolism;Signal Transduction
Conjugation: Unconjugated
Host: Rabbit
Species reactivity: Human;Mouse;Rat
Application: WB;IHC
Isotype: IgG
Clonality: Polyclonal
Clone NO.:
UNIProt ID: Q02252
Accession:
Background: This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.
Concentration: 0.4 mg/mL
Immunogen: Recombinant protein of human ALDH6A1
Buffer: PBS with 0.05% sodium azide and 50% glycerol, PH7.4
Purification method: Affinity purification
Dilution: WB 1:500-1:2000;IHC 1:50-1:200
Calculated MW: 58kDa
ObservedMW:
