GeneBio Systems
ALDH6A1 Polyclonal Antibody
ALDH6A1 Polyclonal Antibody
SKU:E-AB-10769
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Size::120μL
Storage:Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.
Shipping:The product is shipped with ice pack,upon receipt,store it immediately at the temperature recommended.
Exp date:12 months
Category ID_II:Primary Antibodies
Category ID_III:Polyclonal Antibodies
Abbreviation:ALDH6A1
Target Synonym:1110038I05Rik;AI314632;Aldehyde dehydrogenase 6 family member A1;Aldehyde dehydrogenase family 6 member A1;Aldehyde dehydrogenase family 6;subfamily A1;ALDH6A1;Malonate semialdehyde dehydrogenase;Malonate-semialdehyde dehydrogenase [acylating];Methylmalonate semialdehyde dehydrogenase [acylating] mitochondrial;Methylmalonate-semialdehyde dehydrogenase [acylating];MGC37325;MGC40271;Mitochondrial acylating methylmalonate semialdehyde dehydrogenase;mitochondrial;MMSA;MMSADHA;MMSDH
Research Areas:Cancer;Metabolism;Signal Transduction
Conjugation:Unconjugated
Host:Rabbit
Species reactivity:Human;Mouse;Rat
Application:WB;IHC
Isotype:IgG
Clonality:Polyclonal
Clone NO.:
UNIProt ID:Q02252
Accession:
Background:This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.
Concentration:0.4 mg/mL
Immunogen:Recombinant protein of human ALDH6A1
Buffer:PBS with 0.05% sodium azide and 50% glycerol, PH7.4
Purification method:Affinity purification
Dilution:WB 1:500-1:2000;IHC 1:50-1:200
Calculated MW:58kDa
ObservedMW:
